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| Liver transplantation in a patient with massive polycystic liver disease |
| Zhe Yang a , Bulat Abdrakhimov b , Shuo Wang a , Qin-Fen Xie a , Li Zhuang a , Shu-Sen Zheng a , ∗ |
a Department of Hepatobiliary and Pancreatic Surgery, Department of Liver Transplantation, Shulan (Hangzhou) Hospital, Hangzhou 310022, China
b Zhejiang University School of Medicine, Hangzhou 310000, China
∗ Corresponding author.
E-mail address: zyzss@zju.edu.cn (S.-S. Zheng). |
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Abstract Polycystic liver disease (PLD) is a genetic disorder [1] that is diagnosed by presence of multiple hepatic cysts. Clinical manifestations of PLD are related to the size of hepatic cysts and associated complications. In the early stage, PLD rarely causes any symptoms. However, patients with advanced stage PLD have a variety of clinical manifestations and complications due to severe hepatomegaly. They include abdominal pain, abdominal distension, dyspepsia, ascites and many others that may result from compression of adjacent tissue or organ failure [2,3]. Surgical treatment of PLD includes: aspiration with or without sclerotherapy, cyst fenestration, hepatectomy and liver transplantation. Despite some researchers have concluded that cyst fenestration or hepatectomy is effective in treatment of PLD [4–6], the only curative surgical option in severe patients is liver transplantation [7,8]. All other types of surgeries present a great challenge to a surgeon, having little or no effect when cysts are diffuse, or even contraindicated due to possibility of life-threatening complications arising during or after the procedure. Herein, we report a case of 51-year-old male diagnosed with massive PLD complicated by abdominal adhesion, liver cirrhosis, splanchnic varices and ascites that successfully underwent liver transplantation.
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2020, Vol. 19 
