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| Deceased donor liver transplantation for Budd–Chiari syndrome: Long-segmental thrombosis of the inferior vena cava with extensive collateral circulation |
| Zi-Xi Liu # , Ji-Qiao Zhu # , Jun Ma, Jian-Tao Kou, Xian-Liang Li, Qiang He ∗ |
Department of Hepatobiliary and Pancreaticosplenic Surgery, Beijing Chaoyang Hospital, Capital Medical University, No. 8 Gongtinan Road, Chaoyang
District, Beijing 100020, China
∗ Corresponding author.
E-mail address: heqiang349@sina.com (Q. He).
# Contributed equally. |
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Abstract Budd–Chiari syndrome (BCS) is an infrequent clinical disease resulting from obstruction of the hepatic venous outflow tract anywhere from small hepatic veins to the inferior vena cava (IVC) [1] . Currently, step-wise treatment strategy has been proposed and widely adopted based on the patient’s status, which contains anticoagulation, thrombolysis, percutaneous recanalization, transjugular intrahepatic portosystemic shunt (TIPS) and surgical shunt [2] . It has been reported that up to 10%−20% of BCS patients still develop into liver function failure after the step-wise treatment [3] . Therefore, liver transplantation is the remaining rescue treatment in these patients. The five-year survival rate of BCS patients who underwent liver transplantation can reach as high as 80% [4,5] . Notably, very few BCS patients have been reported to have a long-segmental thrombus of IVC. Herein, we presented a patient with total obstruction of the IVC blocked by a longsegmental thrombus, where the common iliac veins and the renal veins were drained into the superior vena cava smoothly through collateral circulation.
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2020, Vol. 19 
