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| Right hepatectomy with a cholangiojejunostomy and hepaticojejunostomy for unilobar Caroli’s syndrome |
| Duminda Subasinghe a , b , ∗, Sivasuriya Sivaganesh a , b |
a Division of HPB Surgery, Department of Surgery, Faculty of Medicine, University of Colombo, Colombo, 00800, Sri Lanka
b The University Surgical Unit, The National Hospital of Sri Lanka, Colombo, 00800, Sri Lanka
∗ Corresponding author at: Division of HPB Surgery, Department of Surgery, Faculty of Medicine, University of Colombo, No. 25, P.O. Box 271, Kynsey Road, Colombo 00800, Sri Lanka.
E-mail address: dumindas1982@yahoo.com (D. Subasinghe). |
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Abstract Choledochal cysts are benign cystic dilatations of the extra- and intrahepatic bile ducts [ 1 , 2 ]. If untreated, their sequelae include recurrent cholangitis, secondary biliary cirrhosis, acute pancreatitis, and cholangiocarcinoma [ 3 , 4 ]. Todani et al. [5] classified choledochal cysts into 5 subtypes, of which type V is Caroli’s disease. The disease is either localized, where unilobar biliary dilatation, commonly in the left, is present, or diffuse, where the entire liver is involved. The surgical treatment of Caroli’s disease depends on the pattern of duct involvement and involves hemi-hepatectomy and liver transplantation. A partial hepatectomy is the best curative option in unilobar disease, providing long-term survival, free of symptoms and complications [4] . Caroli’s syndrome is defined as Caroli’s disease with congenital hepatic fibrosis [6] . Herein, we describe a patient with unilobar Caroli’s syndrome treated for septic complications, who subsequently had a right hepatectomy and complex bilioenteric anastomosis.
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2023, Vol. 22 
